1 例临床诊断新生儿色素失禁症及文献回顾
摘要
皮疹进行性加重，呈 Blaschko 线分布。病初四肢肘膝关节伸侧见红色斑疹，逐渐加重表现为疱疹，疱疹疹结痂后遗留色素
沉着。生后半月龄开始发现头皮疱疹。其辅助检查颅脑磁共振提示斑片状异常病变，诊断主要依据特征性皮疹以及颅脑改
变做出临床诊断。治疗为外涂莫匹罗星预防抗感染，破溃皮疹暴露干燥护理，避免光热刺激。住院治疗 7 天，无新发皮疹
出院。生后 3 个月内皮疹反复，自行对症处理，6 月龄随诊时已无新发皮疹，表现为浅褐色色素沉着。
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